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Many inborn errors of metabolism are characterized by a change in the amount of glucose and...

Many inborn errors of metabolism are characterized by a change in the amount of glucose and ketone bodies in the bloodstream. Two of these disorders affect liver enzymes; Carnitine palmitoyl transferase deficiency and glycogen synthase deficiency. Both disorders lead to hypoglycemia but only one is also associated with hypoketotic hypoglycemia. Explain why both disorders lead to hypoglycemia and which disorder would also result in reduced ketone body synthesis.

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